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An official publication of the ACR and the ARP serving rheumatologists and rheumatology professionals

A Mystery Case of Abdominal Masses

Vania Lin, MD, MPH, Robert Odrobina, MD, Maria A. Pletneva, MD, PhD, & Dorota Lebiedz-Odrobina, MD, RhMSUS  |  Issue: May 2021  |  

Conclusion

The uncommon presentation of granulomatous disease among CVID patients, as well as the consideration of alternative or overlapping infectious, autoimmune or malignant etiologies, poses a diagnostic and treatment challenge. Given the potential for poor outcomes—including infection, unnecessary procedures and progression of disease—with delayed recognition, misdiagnosis or inappropriate treatment, consideration of an immunodeficiency disease is of high importance when approaching a patient with granulomatous disease.

Vania Lin, MD, MPHVania Lin, MD, MPH, is an internal medicine resident at the University of Nevada, Reno, School of Medicine. She plans to pursue a fellowship in rheumatology.

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Dr. OdrobinaRobert Odrobina, MD, is an assistant professor in the Division of Infectious Diseases at the University of Utah, Salt Lake City. His main clinical interests include infections in immunocompromised hosts, especially after bone marrow and solid organ transplantation.

DR. PletnevaMaria A. Pletneva, MD, PhD, is a gastrointestinal pathologist in the Department of Pathology at the University of Utah.

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Dorota Lebiedz-Odrobina, MD, RhMSUSDorota Lebiedz-Odrobina, MD, RhMSUS, is an assistant professor in the Department of Medicine and rheumatology fellowship program director at the University of Utah.

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