Case Report: Child Develops Coronary Artery Aneurysms with GPA

1. ANCA-associated vasculitis should be considered in children with coronary artery aneur­ysms, especially if their presentation is atypical for Kawasaki disease;
2. The clinician who suspects or diagnoses an ANCA-associated vasculitis in a pediatric patient should consider coronary artery aneurysms as a possible and dangerous sequela; and
3. Coronary artery aneurysms should be included in the PVAS scoring criteria.

Tryphina Adel Mikhail has a B.S. in Biomedical Sciences and is a fourth-year medical student at the University of Central Florida College of Medicine, Orlando. She plans to pursue a career in pediatrics and medical education.

Mary Bratovich Toth, MD, is a professor of pediatrics at the University of Central Florida College of Medicine and the pediatric rheumatology division chief for Nemours Children’s Hospital, Orlando. She is faculty for the adult rheumatology fellowship at the University of Central Florida and active in CARRA (Childhood Arthritis and Rheumatology Research Alliance).

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