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An official publication of the ACR and the ARP serving rheumatologists and rheumatology professionals

Diffuse Scleroderma: A 1991 Case Through the Lens of Today

Charles Radis, DO  |  Issue: February 2018  |  

I remember Dr. Indura. The answers can’t come soon enough.

Charles Radis, DO, is clinical professor of medicine at the University of New England, College of Osteopathic Medicine and employed part time at Maine Coast Memorial Hospital in Ellsworth, Maine.

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References

  1. Traub YM, Shapiro AP, Rodnan GP, Medsger TA. Hypertension and renal failure (scleroderma renal crisis) in progressive systemic sclerosis. Review of a 25-year experience with 68 cases. Medicine. 1983 Nov;62(6):335–352.
  2. Nietert PJ, Sutherland SE, Silver RM, et al. Is occupational organic solvent exposure a risk factor for scleroderma? Arthritis Rheum. 1998 Jun;41(6):1111–1118.
  3. Belongia EA, Hedberg CW, Gleich GJ, et al. An investigation of the cause of the eosinophilia–myalgia syndrome associated with tryptophan use. New Engl J Med. 1990 Aug 9;323(6):357–365.
  4. Hill RH Jr., Caudill SP, Philen RM, et al. Contaminants in L-tryptophan associated with eosinophilia myalgia syndrome. Arch Environ Contam Toxicol. 1993 Jul;25(1):134–142.
  5. Mayes MD, Lacey JV Jr., Beebe-Dimmer J, et al. Prevalence, incidence, survival, and disease characteristics of systemic sclerosis in a large US population. Arthritis Rheum. 2003 Aug;48(8):2246–2255.
  6. Artlett CM, Smith JB, Jimenez SA. Identification of fetal DNA and cells in skin lesions from women with systemic sclerosis. N Engl J Med. 1998 Apr 23;338(17):1186–1191.
  7. Khanna D, Denton CP, Jahreis A, et al. Safety and efficacy of subcutaneous tocilizumab in adults with systemic sclerosis (faSScinate): A phase 2, randomised, controlled trial. Lancet. 2016 Jun 25;387(10038):2630–2640.
  8. Khanna D, Denton CP, Lin CJF, et al. Safety and efficacy of subcutaneous tocilizumab in systemic sclerosis: Results from the open-label period of a phase II randomised controlled trial (faSScinate). Ann Rheum Dis. 2018 Feb;77(2):212–220.
  9. Sullivan KM, Goldmuntz EA, Keyes-Elstein L, et al. Myeloablative autologous stem-cell transplantation for severe scleroderma. New Engl J Med. 2018 Jan 4;378(1):35–47.

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